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Universidad y Salud
Print version ISSN 0124-7107On-line version ISSN 2389-7066
Abstract
PAZ-MONTANEZ, John Jamer; GAITAN-GUZMAN, Luisa Fernanda and ACOSTA-ARAGON, María Amparo. A case of OHVIRA syndrome. Univ. Salud [online]. 2020, vol.22, n.3, pp.288-291. Epub Sep 01, 2020. ISSN 0124-7107. https://doi.org/10.22267/rus.202203.201.
Introduction:
The obstructed hemivagina and ipsilateral renal anomaly (OHVIRA) syndrome, also known as the Herlyn-Werner-Wunderlich syndrome, is a rare müllerian anomaly characterized by didelphic uterus, hemivaginal obstruction, and ipsilateral renal anomaly. The incidence of müllerian malformations is 2% - 3%, OHVIRA being the least common of these cases.
Objective:
To describe an exceptional case of a müllerian disorder.
Case presentation:
A 14-year-old adolescent with a history of pelvic pain, dysmenorrhea, and recurrent urinary infections. Renal gammagraphy analysis revealed right renal agenesis, and pelvic magnetic resonance imaging showed a didelphic uterus with right hematocolpos. These findings were confirmed by diagnostic laparoscopy.
Conclusions:
This syndrome is not well known. Renal anegesis, chronic pelvic pain, and menstrual abnormalities in post-pubertal patients must be presumed as indicators of OHVIRA, whose treatment requires a multidisciplinary approach.
Keywords : Uterine hemorrhage; urogenital abnormalities; solitary kidney.