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Revista Colombiana de Cardiología
Print version ISSN 0120-5633
Abstract
MOSQUERA, Walter; ARISTIZABAL, Ana M. and PINTO, Iván. Unusual presentation of Lutembachers syndrome. Rev. Colomb. Cardiol. [online]. 2022, vol.29, suppl.4, pp.1-4. Epub Dec 20, 2022. ISSN 0120-5633. https://doi.org/10.24875/rccar.m22000196.
Introduction:
Lutembachers syndrome corresponds to the association of an atrial septal defect (congenital or iatrogenic) and mitral regurgitation or stenosis (congenital or acquired), with rheumatic etiology being the most-frequent cause of mitral regurgitation. It has a reported prevalence of 0.001 for every 1,000,000 inhabitants.
Clinical case:
Female patient six years of age with a 10-month condition of palpitations associated with chest pain. An electrocardiogram was performed with evidence of incomplete right His bundle branch block and PR interval prolongation; additionally, an echocardiogram showed 28-mm non-restrictive ostium secundum atrial septal defect, with left-to-right shunt, right ventricular dilation, mitral valve prolapse, thickened valves, and moderate-to-severe mitral regurgitation. Mitral valve plasty and surgical closure of the atrial septal defect were performed, without complications. During follow-up, she was asymptomatic from the cardiovascular point of view, under pharmacological management.
Conclusions:
Lutembachers association has a prevalence of 0.001/1´000.000 inhabitants; the majority with rheumatic etiology. Our patient has no history of rheumatic fever and would be the youngest patient reported in the literature with Lutembachers syndrome.
Keywords : Atrial septal defect; Mitral valve regurgitation; Lutembachers syndrome; Mitral valve prolapse.