Abstract

RIOS-DUENAS, Giovanny; GALAN-CADENA, José A.; OLMOS-MUSKUS, Natalia  and  RIVERA-TOBAR, Isabella. Right ventricular double outlet dextrocardia with unrelated ventricular septal defect associated with great vessel malposition. Rev. Colomb. Cardiol. [online]. 2021, vol.28, n.4, pp.383-388.  Epub Oct 18, 2021. ISSN 0120-5633.  https://doi.org/10.24875/rccar.m21000070.

The following report presents a complex case in which congenital cardiac malformations of atypical presentation coexist with a double outlet right ventricle, in a patient with multiple minor abnormalities on the physical examination and a normal karyotype. The atypia of these and their coexistence suggest possible genetic alterations that are still unknown. Therefore, a therapeutic challenge in order to restore a cardiac physiology compatible with life is proposed, which is achieved in this case through a successful banding of the pulmonary artery.

Keywords : Double outlet right ventricle; Dextrocardia; Pulmonary hypertension; Pulmonary artery.

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