Abstract

ORTEGA ESPINOSA, César Ricardo  and  SALDARRIAGA RIVERA, Lina Maria. Presentation of Idiopathic Portal Hypertension in a Patient with Limited Systemic Sclerosis. Rev Col Gastroenterol [online]. 2014, vol.29, n.3, pp.276-280. ISSN 0120-9957.

Systemic sclerosis is a multisystem rheumatic autoimmune disorder characterized by fibrosis of the skin and many other organs. The gastrointestinal tract is the second cause of systemic compromise of this disease, but idiopathic portal hypertension is an extremely rare condition in these patients. We describe the case of a female patient with atypical hepatic changes of idiopathic portal hypertension associated with limited systemic sclerosis. Since these entities rarely coexist in the same individual, and since this is the first clinical association in our environment, we present this literature review and case report.

Keywords : Systemic sclerosis; portal hypertension; liver disease.

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