Resumen

SALDARRIAGA G, Wilmar. Pentalogy of Cantrell. Case report. Salud, Barranquilla [online]. 2014, vol.30, n.3, pp.505-512. ISSN 0120-5552.

The pentalogy of Cantrell is a congenital anomaly characterized by variable association of a thoracoabdominal wall defect to defect of the lower sternum, diaphragm, pericardium and heart, the most representative is ectopia cordis. Cantrell in 1958 reported 5 cases with this anomaly. The prevalence of pentalogy of Cantrell has been estimated between 1 /65,000 to 1 in 200,000 live births. The etiology of this anomaly is not clear and is considered heterogeneous. The mechanism proposed embriopatológico suggests aflaw in the ventral migration of mesodermal cells. We report a case of pentalogy of Cantrell with all the classic features with prenatal diagnosis. It also suggests a hypothesis about the embriopatogénesis and integrated management of the mother and fetus.

Palabras clave : Pentalogy of Cantrell.

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